Vol.100 No.9 contentsPRACTICA OTO-RHINO-LARYNGOLOGICA
Vol. 100 No. 9 September 2007
First and Second Branchial Arch Syndrome with
Fistula Originated from First Pharyngeal Pouch
Tadashi Wada, Takafumi Togashi, Masaaki Ono,
Kunihiro Sato and Sugata Takahashi
(Niigata University)
Satoshi Seki
(Shibata City)
We report a rare case of first and second branchial arch syndrome with fistula originated from the first pharyngeal pouch. A 10-day-old female was referred to our clinic with a complaint of left microtia with fistula at the mandibular angle. On preoperative examinations, X-ray with angiography flexible wire inserted into the fistula and computed tomography with contrast enhancement of the fistula revealed that the fistula was connected to the middle ear cavity. Fistulectomy was performed at the age of 7. Pathological examinations demonstrated that the fistula consisted of a single layer of cylindrical epithelium, suggesting that it originated from the endoderm. Based on surgical, imaging, and pathological findings, the fistula originated from first pharyngeal pouch. Preoperative X-ray with angiography flexible wire inserted into the fistula and the computed tomography with contrast enhancement of the fistula were useful for planning operation.
Key words : first pharyngeal pouch, fistula, first and second branchial arch syndrome