PRACTICA OTO-RHINO-LARYNGOLOGICA
Vol. 103 No. 1 January 2010
A Case of Superficial Central Nervous System Siderosis Exhibiting Vertigo
Hisashi Ohtsuka, Chigumi Ohtsuka, Hisashi Yonezawa,
Masaru Tateda, Ken Ishijima and Hiroaki Sato
(Iwate Medical University)
Superficial central nervous system siderosis is a very rare disease related to hemosiderin deposits in the brain, brain stem, cerebellum, and spinal cord due to chronic subarachnoid hemorrhage. Clinical findings are progressive bilateral sensorineural hearing loss, cerebellar ataxia, and pyramidal tract signs. A 62-year-old woman exhibited vertigo, worsening tinnitus, unstable gait, and spontaneous Bruns-like horizontal nystagmus. A central nervous system disorder was suspected due to the vertical vector that emerged when the woman looked upward. Magnetic resonance imaging (MRI) showed a low-intensity rim in T2-weighted imaging enveloping the brain and spinal cord surface.
Key words :superficial central nervous system siderosis, vertigo