Vol.97 No.4 contentsPRACTICA OTO-RHINO-LARYNGOLOGICA
Vol. 97 No. 4 April 2004
An Intractable Case of Kasabach-Merritt Syndrome
with Neck Hemangioma in Infant
Sachio Tsuda, Hirohito Umeno and Tadashi Nakashima
(Kurume University)
We report an intractable case of Kasabach-Merritt syndrome with neck hemangioma in an infant. A four-month-old girl presented with hemangioma of the right neck and thrombocytopenia known as Kasabach-Merritt syndrome. It is the most common vascular disease in the pediatric age group. Initially, we treated the hemangioma with steroid (predonisolone), surgery and embolization.
However each therapy was unsuccessful, and therfore we finally treated the patient with radiation therapy (9 Gy) and the hemangioma was well controlled.
From our experience, radiation therapy may be effective for hemangioma with Kasabach-Merritt syndrome if the tumor is not completely resected by surgical procedure.
Key words : Kasabach-Merritt syndrome, hemangioma, radiation therapy